Ernesto R. Bongarzone

Publications

• Aberrant Production of Tenascin-C in Globoid Cell Leukodystrophy Alters Psychosine-induced Microglial Functions
  Journal of Neuropathology and Experimental Neurology. Oct, 2014  |   Pubmed ID: 25192051
• Vitamin C Transporters, Recycling and the Bystander Effect in the Nervous System: SVCT2 Versus Gluts
  Journal of Stem Cell Research & Therapy. May, 2014  |   Pubmed ID: 25110615
• Neuronal Inclusions of α-synuclein Contribute to the Pathogenesis of Krabbe Disease
  The Journal of Pathology. Apr, 2014  |   Pubmed ID: 24415155
• Characterization and Application of a Disease-cell Model for a Neurodegenerative Lysosomal Disease
  Molecular Genetics and Metabolism. Feb, 2014  |   Pubmed ID: 24094551
• Inhibition of Angiogenesis by β-galactosylceramidase Deficiency in Globoid Cell Leukodystrophy
  Brain : a Journal of Neurology. Sep, 2013  |   Pubmed ID: 23983033
• The Sphingolipid Psychosine Inhibits Fast Axonal Transport in Krabbe Disease by Activation of GSK3β and Deregulation of Molecular Motors
  The Journal of Neuroscience : the Official Journal of the Society for Neuroscience. Jun, 2013  |   Pubmed ID: 23761900
• Missense Mutation in Mouse GALC Mimics Human Gene Defect and Offers New Insights into Krabbe Disease
  Human Molecular Genetics. Sep, 2013  |   Pubmed ID: 23620143
• MMP-3 Mediates Psychosine-induced Globoid Cell Formation: Implications for Leukodystrophy Pathology
  Glia. May, 2013  |   Pubmed ID: 23404611
• Detection of the Neurotoxin Psychosine in Samples of Peripheral Blood: Application in Diagnostics and Follow-up of Krabbe Disease
  Archives of Pathology & Laboratory Medicine. Jul, 2012  |   Pubmed ID: 22742542
• Psychosine Induces the Dephosphorylation of Neurofilaments by Deregulation of PP1 and PP2A Phosphatases
  Neurobiology of Disease. May, 2012  |   Pubmed ID: 22326830
• Peripheral Neuropathy in the Twitcher Mouse Involves the Activation of Axonal Caspase 3
  ASN Neuro. 2011  |   Pubmed ID: 21929508
• Psychosine Accumulates in Membrane Microdomains in the Brain of Krabbe Patients, Disrupting the Raft Architecture
  The Journal of Neuroscience : the Official Journal of the Society for Neuroscience. May, 2009  |   Pubmed ID: 19439584
• P2x7 Deficiency Suppresses Development of Experimental Autoimmune Encephalomyelitis
  Journal of Neuroinflammation. 2008  |   Pubmed ID: 18691411
• Autonomic Denervation of Lymphoid Organs Leads to Epigenetic Immune Atrophy in a Mouse Model of Krabbe Disease
  The Journal of Neuroscience : the Official Journal of the Society for Neuroscience. Dec, 2007  |   Pubmed ID: 18077684
• Effects of Irradiation on the Postnatal Development of the Brain in a Genetic Mouse Model of Globoid Cell Leukodystrophy
  Neurochemical Research. Feb, 2007  |   Pubmed ID: 17203404
• Neural Stem/progenitor Cells Participate in the Regenerative Response to Perinatal Hypoxia/ischemia
  The Journal of Neuroscience : the Official Journal of the Society for Neuroscience. Apr, 2006  |   Pubmed ID: 16624956
• Notch Signaling in Astrocytes and Neuroblasts of the Adult Subventricular Zone in Health and After Cortical Injury
  Developmental Neuroscience. 2006  |   Pubmed ID: 16508306
• Axons Mediate the Distribution of Arylsulfatase A Within the Mouse Hippocampus Upon Gene Delivery
  Molecular Therapy : the Journal of the American Society of Gene Therapy. Oct, 2005  |   Pubmed ID: 16087406
• Embryonic Expression of the Soma-restricted Products of the Myelin Proteolipid Gene in Motor Neurons and Muscle
  Neurochemical Research. May, 2004  |   Pubmed ID: 15139298
• Identification of a Protein That Interacts with the Golli-myelin Basic Protein and with Nuclear LIM Interactor in the Nervous System
  Journal of Neuroscience Research. Feb, 2004  |   Pubmed ID: 14743429
• Expression of Soma-restricted Proteolipid/DM20 Proteins in Lymphoid Cells
  Journal of Neuroimmunology. Nov, 2003  |   Pubmed ID: 14597093
• Soma-restricted Products of the Myelin Proteolipid Gene Are Expressed Primarily in Neurons in the Developing Mouse Nervous System
  Developmental Neuroscience. Mar-Aug, 2003  |   Pubmed ID: 12966208
• Notch1 and Numb Genes Are Inversely Expressed As Oligodendrocytes Differentiate
  Developmental Neuroscience. Jan-Feb, 2003  |   Pubmed ID: 12876431
• Induction of Oligodendrocyte Fate During the Formation of the Vertebrate Neural Tube
  Neurochemical Research. Nov, 2002  |   Pubmed ID: 12512941
• Myelin: Development, Disorders and Neural Repair. A Satellite Meeting of the International and American Societies for Neurochemistry Joint Meeting in Buenos Aires. Bastion Del Carmen, September 1-4, 2001, Colonia, Uruguay
  Journal of Neuroscience Research. Apr, 2002  |   Pubmed ID: 11933056
• Central Nervous System Myelination in Mice with Deficient Expression of Notch1 Receptor
  Journal of Neuroscience Research. Feb, 2002  |   Pubmed ID: 11813235