Isabelle Sermet-Gaudelus Institut Necker Enfants Malades Biography Publications Institution JoVE Articles Isabelle Sermet-Gaudelus has not added a biography. If you are Isabelle Sermet-Gaudelus and would like to personalize this page please email our Author Liaison for assistance. Publications Systemic Bis-phosphinic Acid Derivative Restores Chloride Transport in Cystic Fibrosis Mice Scientific Reports. Apr, 2022 | Pubmed ID: 35413967 A Phase 3, Open-label, 96-week Trial to Study the Safety, Tolerability, and Efficacy of Tezacaftor/ivacaftor in Children ≥ 6 Years of Age Homozygous for F508del or Heterozygous for F508del and a Residual Function CFTR Variant Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Feb, 2022 | Pubmed ID: 35190292 Comparison of Transient Elastography, ShearWave Elastography, Magnetic Resonance Elastography and FibroTest As Routine Diagnostic Markers for Assessing Liver Fibrosis in Children with Cystic Fibrosis Clinics and Research in Hepatology and Gastroenterology. 03, 2022 | Pubmed ID: 34933150 Correlating Genotype with Phenotype Using CFTR-mediated Whole-cell Cl Currents in Human Nasal Epithelial Cells The Journal of Physiology. Mar, 2022 | Pubmed ID: 34761808 Lumacaftor-ivacaftor Effects on Cystic Fibrosis-related Liver Involvement in Adolescents with Homozygous F508 Del-CFTR Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 03, 2022 | Pubmed ID: 34454846 Reclassifying Inconclusive Diagnosis After Newborn Screening for Cystic Fibrosis. Moving Forward Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Dec, 2021 | Pubmed ID: 34949556 Inflammation Biomarkers in Sputum for Clinical Trials in Cystic Fibrosis: Current Understanding and Gaps in Knowledge Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Nov, 2021 | Pubmed ID: 34772643 Pharmacological Chaperones Improve Intra-domain Stability and Inter-domain Assembly Via Distinct Binding Sites to Rescue Misfolded CFTR Cellular and Molecular Life Sciences : CMLS. Dec, 2021 | Pubmed ID: 34714360 Author Correction: New Insights into Structure and Function of Bis-phosphinic Acid Derivatives and Implications for CFTR Modulation Scientific Reports. Sep, 2021 | Pubmed ID: 34526640 Therapeutic Pipeline for Individuals with Cystic Fibrosis with Mutations Nonresponsive to Current Cystic Fibrosis Transmembrane Conductance Regulator Modulators Current Opinion in Pulmonary Medicine. 11, 2021 | Pubmed ID: 34494979 Sweat Chloride Testing and Nasal Potential Difference (NPD) Are Primary Outcome Parameters in Treatment with Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulators Journal of Personalized Medicine. Jul, 2021 | Pubmed ID: 34442373 Insights Into Patient Variability During Ivacaftor-Lumacaftor Therapy in Cystic Fibrosis Frontiers in Pharmacology. 2021 | Pubmed ID: 34408649 Antisense Oligonucleotide-based Drug Development for Cystic Fibrosis Patients Carrying the 3849+10 kb C-to-T Splicing Mutation Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 09, 2021 | Pubmed ID: 34226157 Involvement of CFTR in the Pathogenesis of Pulmonary Arterial Hypertension The European Respiratory Journal. 11, 2021 | Pubmed ID: 33926975 Airway Surface Liquid PH Regulation in Airway Epithelium Current Understandings and Gaps in Knowledge International Journal of Molecular Sciences. Mar, 2021 | Pubmed ID: 33806154 Prior Infection by Seasonal Coronaviruses, As Assessed by Serology, Does Not Prevent SARS-CoV-2 Infection and Disease in Children, France, April to June 2020 Euro Surveillance : Bulletin Europeen Sur Les Maladies Transmissibles = European Communicable Disease Bulletin. 04, 2021 | Pubmed ID: 33797390 New Insights into Structure and Function of Bis-phosphinic Acid Derivatives and Implications for CFTR Modulation Scientific Reports. 03, 2021 | Pubmed ID: 33767236 "Il Faut Continuer à Poser Des Questions" Patient Reported Outcome Measures in Cystic Fibrosis: An Anthropological Perspective Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 11, 2021 | Pubmed ID: 33648900 Modulators of CFTR. Updates on Clinical Development and Future Directions European Journal of Medicinal Chemistry. Mar, 2021 | Pubmed ID: 33524685 Pharmacokinetic and Pharmacodynamic Optimization of Antibiotic Therapy in Cystic Fibrosis Patients: Current Evidences, Gaps in Knowledge and Future Directions Clinical Pharmacokinetics. 04, 2021 | Pubmed ID: 33486720 Arterial Abnormalities Identified in Kidneys Transplanted into Children During the COVID-19 Pandemic American Journal of Transplantation : Official Journal of the American Society of Transplantation and the American Society of Transplant Surgeons. 05, 2021 | Pubmed ID: 33346946 Exon Identity Influences Splicing Induced by Exonic Variants and in Silico Prediction Efficacy Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 05, 2021 | Pubmed ID: 33341408 Updated Guidance on the Management of Children with Cystic Fibrosis Transmembrane Conductance Regulator-related Metabolic Syndrome/cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CRMS/CFSPID) Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 09, 2021 | Pubmed ID: 33257262 A Phase 3, Double-blind, Parallel-group Study to Evaluate the Efficacy and Safety of Tezacaftor in Combination with Ivacaftor in Participants 6 Through 11 Years of Age with Cystic Fibrosis Homozygous for F508del or Heterozygous for the F508del-CFTR Mutation and a Residual Function Mutation Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 01, 2021 | Pubmed ID: 32967799 Clinical Response to Lumacaftor-ivacaftor in Patients with Cystic Fibrosis According to Baseline Lung Function Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 03, 2021 | Pubmed ID: 32591294 Urinary Exosomes of Patients with Cystic Fibrosis Unravel CFTR-Related Renal Disease International Journal of Molecular Sciences. Sep, 2020 | Pubmed ID: 32927759 Impact of COVID-19 on People with Cystic Fibrosis The Lancet. Respiratory Medicine. 05, 2020 | Pubmed ID: 32304639 Suppressing 'nonsense' in Cystic Fibrosis The Journal of Physiology. 02, 2020 | Pubmed ID: 31869855 CFTR: New Insights into Structure and Function and Implications for Modulation by Small Molecules Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 03, 2020 | Pubmed ID: 31759907 Insights into the Variability of Nasal Potential Difference, a Biomarker of CFTR Activity Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 07, 2020 | Pubmed ID: 31699569 Real-Life Safety and Effectiveness of Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis American Journal of Respiratory and Critical Care Medicine. 01, 2020 | Pubmed ID: 31601120 A Critical Review of Definitions Used to Describe Pseudomonas Aeruginosa Microbiological Status in Patients with Cystic Fibrosis for Application in Clinical Trials Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 01, 2020 | Pubmed ID: 31526710 Author Correction: Airway Surface Liquid Acidification Initiates Host Defense Abnormalities in Cystic Fibrosis Scientific Reports. Nov, 2019 | Pubmed ID: 31754179 Cystic Fibrosis Bone Disease Treatment: Current Knowledge and Future Directions Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 10, 2019 | Pubmed ID: 31679730 Cystic Fibrosis Diagnosis in Newborns, Children, and Adults Seminars in Respiratory and Critical Care Medicine. 12, 2019 | Pubmed ID: 31679154 Airway Surface Liquid Acidification Initiates Host Defense Abnormalities in Cystic Fibrosis Scientific Reports. 04, 2019 | Pubmed ID: 31019198 Mycobacterium Bolletii Lung Disease In Cystic Fibrosis Chest. 08, 2019 | Pubmed ID: 30935892 Emerging Therapeutic Approaches for Cystic Fibrosis. From Gene Editing to Personalized Medicine Frontiers in Pharmacology. 2019 | Pubmed ID: 30873022 Chronic Staphylococcus Aureus Lung Infection Correlates With Proteogenomic and Metabolic Adaptations Leading to an Increased Intracellular Persistence Clinical Infectious Diseases : an Official Publication of the Infectious Diseases Society of America. 11, 2019 | Pubmed ID: 30753350 Predictive Factors for Lumacaftor/ivacaftor Clinical Response Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 05, 2019 | Pubmed ID: 30595473 Might Brushed Nasal Cells Be a Surrogate for CFTR Modulator Clinical Response? American Journal of Respiratory and Critical Care Medicine. 01, 2019 | Pubmed ID: 30326728 Increased Expression of ATP12A Proton Pump in Cystic Fibrosis Airways JCI Insight. 10, 2018 | Pubmed ID: 30333310 Structure-guided Combination Therapy to Potently Improve the Function of Mutant CFTRs Nature Medicine. 11, 2018 | Pubmed ID: 30297908 Correction To: In Vitro Prediction of Stop-codon Suppression by Intravenous Gentamicin in Patients with Cystic Fibrosis: a Pilot Study BMC Medicine. 08, 2018 | Pubmed ID: 30143037 N1303K: Leaving No Stone Unturned in the Search for Transformational Therapeutics Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 09, 2018 | Pubmed ID: 30126793 ECFS Best Practice Guidelines: the 2018 Revision Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Mar, 2018 | Pubmed ID: 29506920 Factors Influencing Readthrough Therapy for Frequent Cystic Fibrosis Premature Termination Codons ERJ Open Research. Jan, 2018 | Pubmed ID: 29497617 Cis Variants Identified in F508del Complex Alleles Modulate CFTR Channel Rescue by Small Molecules Human Mutation. 04, 2018 | Pubmed ID: 29271547 Multifocal Fixed Drug Eruption to Ceftazidime in a Child with Cystic Fibrosis Pediatric Allergy and Immunology : Official Publication of the European Society of Pediatric Allergy and Immunology. 02, 2018 | Pubmed ID: 29047164 Guidelines for the Clinical Management and Follow-up of Infants with Inconclusive Cystic Fibrosis Diagnosis Through Newborn Screening Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Dec, 2017 | Pubmed ID: 29174009 The Suppression of Premature Termination Codons and the Repair of Splicing Mutations in CFTR Current Opinion in Pharmacology. 06, 2017 | Pubmed ID: 29128743 Correction of CFTR Function in Nasal Epithelial Cells from Cystic Fibrosis Patients Predicts Improvement of Respiratory Function by CFTR Modulators Scientific Reports. Aug, 2017 | Pubmed ID: 28785019 A Multiple Reader Scoring System for Nasal Potential Difference Parameters Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Sep, 2017 | Pubmed ID: 28465124 [Management of Infants Whose Diagnosis is Inconclusive at Neonatal Screening for Cystic Fibrosis] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Apr, 2017 | Pubmed ID: 28258861 Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation The Journal of Pediatrics. Feb, 2017 | Pubmed ID: 28129811 Diagnosis of Cystic Fibrosis in Screened Populations The Journal of Pediatrics. Feb, 2017 | Pubmed ID: 28129810 Changes of CFTR Functional Measurements and Clinical Improvements in Cystic Fibrosis Patients with Non P.Gly551Asp Gating Mutations Treated with Ivacaftor Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 01, 2017 | Pubmed ID: 27659740 French Law: What About a Reasoned Reimbursement of Serum Vitamin D Assays? Geriatrie Et Psychologie Neuropsychiatrie Du Vieillissement. Dec, 2016 | Pubmed ID: 27818369 Bone Demineralization is Improved by Ivacaftor in Patients with Cystic Fibrosis Carrying the P.Gly551Asp Mutation Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 11, 2016 | Pubmed ID: 27745802 Analysis of Nasal Potential in Murine Cystic Fibrosis Models The International Journal of Biochemistry & Cell Biology. 11, 2016 | Pubmed ID: 27717840 Long-Term Rasamsonia Argillacea Complex Species Colonization Revealed by PCR Amplification of Repetitive DNA Sequences in Cystic Fibrosis Patients Journal of Clinical Microbiology. 11, 2016 | Pubmed ID: 27605712 Bioelectrical Impedance in Young Patients with Cystic Fibrosis: Validation of a Specific Equation and Clinical Relevance Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. 11, 2016 | Pubmed ID: 27289197 Lessons from a French Collaborative Case-control Study in Cystic Fibrosis Patients During the 2009 A/H1N1 Influenza Pandemy BMC Infectious Diseases. Feb, 2016 | Pubmed ID: 26830335 US Cystic Fibrosis Foundation and European Cystic Fibrosis Society Consensus Recommendations for the Management of Non-tuberculous Mycobacteria in Individuals with Cystic Fibrosis: Executive Summary Thorax. Jan, 2016 | Pubmed ID: 26678435 US Cystic Fibrosis Foundation and European Cystic Fibrosis Society Consensus Recommendations for the Management of Non-tuberculous Mycobacteria in Individuals with Cystic Fibrosis Thorax. Jan, 2016 | Pubmed ID: 26666259 An Unexpected Effect of TNF-α on F508del-CFTR Maturation and Function F1000Research. 2015 | Pubmed ID: 26594334 Effect of Ivacaftor Treatment in Patients with Cystic Fibrosis and the G551D-CFTR Mutation: Patient-reported Outcomes in the STRIVE Randomized, Controlled Trial Health and Quality of Life Outcomes. Jul, 2015 | Pubmed ID: 26135562 Persistent Bordetella Bronchiseptica Infection in a Child with Cystic Fibrosis: Relationship to Bacterial Phenotype Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Sep, 2015 | Pubmed ID: 25900817 Central Venous Thrombosis and Thrombophilia in Cystic Fibrosis: A Prospective Study Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Jan, 2015 | Pubmed ID: 25107684 Pseudomonas Aeruginosa Eradicates Staphylococcus Aureus by Manipulating the Host Immunity Nature Communications. Oct, 2014 | Pubmed ID: 25290234 [Weakening Osteopathies, Chronic Kidney Disease, Malabsorption, Biological Anomalies of Calium/phosphorus Metabolism: Appropriate Indications for a Reasoned Reimbursment of Serum Vitamin D Measurement] Annales De Biologie Clinique. Jul-Aug, 2014 | Pubmed ID: 25119796 Factors Associated with Humoral Immune Response to Pandemic A/H1N1(v) 2009 Influenza Vaccine in Cystic Fibrosis Vaccine. Jul, 2014 | Pubmed ID: 24950362 European Cystic Fibrosis Society Standards of Care: Best Practice Guidelines Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. May, 2014 | Pubmed ID: 24856775 Ataluren for the Treatment of Nonsense-mutation Cystic Fibrosis: a Randomised, Double-blind, Placebo-controlled Phase 3 Trial The Lancet. Respiratory Medicine. Jul, 2014 | Pubmed ID: 24836205 [National French Guidelines for Management of Infants with Cystic Fibrosis] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Jun, 2014 | Pubmed ID: 24815598 Biosynthesis of Cystic Fibrosis Transmembrane Conductance Regulator The International Journal of Biochemistry & Cell Biology. Jul, 2014 | Pubmed ID: 24685677 Ivacaftor Treatment in Patients with Cystic Fibrosis and the G551D-CFTR Mutation European Respiratory Review : an Official Journal of the European Respiratory Society. Mar, 2013 | Pubmed ID: 23457167 Determinants of Refusal of A/H1N1 Pandemic Vaccination in a High Risk Population: a Qualitative Approach PloS One. 2012 | Pubmed ID: 22506011 Genotypic and Phenotypic Variation in Pseudomonas Aeruginosa Reveals Signatures of Secondary Infection and Mutator Activity in Certain Cystic Fibrosis Patients with Chronic Lung Infections Infection and Immunity. Dec, 2011 | Pubmed ID: 21930755 [French Guidelines for Sweat Test Practice and Interpretation for Cystic Fibrosis Neonatal Screening] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Sep, 2010 | Pubmed ID: 20719482 Ataluren (PTC124) Induces Cystic Fibrosis Transmembrane Conductance Regulator Protein Expression and Activity in Children with Nonsense Mutation Cystic Fibrosis American Journal of Respiratory and Critical Care Medicine. Nov, 2010 | Pubmed ID: 20622033 Guidelines on the Early Management of Infants Diagnosed with Cystic Fibrosis Following Newborn Screening Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Sep, 2010 | Pubmed ID: 20605539 Clinical Phenotype and Genotype of Children with Borderline Sweat Test and Abnormal Nasal Epithelial Chloride Transport American Journal of Respiratory and Critical Care Medicine. Oct, 2010 | Pubmed ID: 20538955 Measurement of Nasal Potential Difference in Young Children with an Equivocal Sweat Test Following Newborn Screening for Cystic Fibrosis Thorax. Jun, 2010 | Pubmed ID: 20522854 An International Randomized Multicenter Comparison of Nasal Potential Difference Techniques Chest. Oct, 2010 | Pubmed ID: 20472865 Update on Cystic Fibrosis-related Bone Disease: a Special Focus on Children Paediatric Respiratory Reviews. Sep, 2009 | Pubmed ID: 19651384 Effect of Mutator P. Aeruginosa on Antibiotic Resistance Acquisition and Respiratory Function in Cystic Fibrosis Pediatric Pulmonology. Aug, 2009 | Pubmed ID: 19598278 [Bone Health in Cystic Fibrosis] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Jun, 2009 | Pubmed ID: 19541106 [Novel Therapies for Cystic Fibrosis in 2009] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Jun, 2009 | Pubmed ID: 19541091 Pain in Children and Adults with Cystic Fibrosis: a Comparative Study Journal of Pain and Symptom Management. 08, 2009 | Pubmed ID: 19364632 Matrix-assisted Laser Desorption Ionization-time of Flight Mass Spectrometry for Identification of Nonfermenting Gram-negative Bacilli Isolated from Cystic Fibrosis Patients Journal of Clinical Microbiology. Oct, 2008 | Pubmed ID: 18685005 Bacterial Contamination in the Environment of Hospitalised Children with Cystic Fibrosis Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society. Nov, 2008 | Pubmed ID: 18550452 [Recommendations for the Management of Bone Demineralization in Cystic Fibrosis] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Mar, 2008 | Pubmed ID: 18325750 [Parvovirus B19: Importance of Diathesis in the Clinical Expression of a Common Infection] La Revue Du Praticien. May, 2007 | Pubmed ID: 17844796 In Vitro Prediction of Stop-codon Suppression by Intravenous Gentamicin in Patients with Cystic Fibrosis: a Pilot Study BMC Medicine. Mar, 2007 | Pubmed ID: 17394637 Low Bone Mineral Density in Young Children with Cystic Fibrosis American Journal of Respiratory and Critical Care Medicine. May, 2007 | Pubmed ID: 17272788 [Anti Pseudomonas Aeruginosa Antibiotic Therapy in Cystic Fibrosis (exclusion of Macrolides)] Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie. Oct, 2006 | Pubmed ID: 17370394 The CF-CIRC Study: a French Collaborative Study to Assess the Accuracy of Cystic Fibrosis Diagnosis in Neonatal Screening BMC Pediatrics. Oct, 2006 | Pubmed ID: 17018149 Myeloperoxidase Promoter Polymorphism -463G is Associated with More Severe Clinical Expression of Cystic Fibrosis Pulmonary Disease Mediators of Inflammation. 2006 | Pubmed ID: 16883063 Value of the Chlorhexidine Decontamination Method for Recovery of Nontuberculous Mycobacteria from Sputum Samples of Patients with Cystic Fibrosis Journal of Clinical Microbiology. Jun, 2006 | Pubmed ID: 16757627 Age-related Prevalence and Distribution of Nontuberculous Mycobacterial Species Among Patients with Cystic Fibrosis Journal of Clinical Microbiology. Jul, 2005 | Pubmed ID: 16000480 Measurement of Immunoglobulin G Against Mycobacterial Antigen A60 in Patients with Cystic Fibrosis and Lung Infection Due to Mycobacterium Abscessus Clinical Infectious Diseases : an Official Publication of the Infectious Diseases Society of America. Jan, 2005 | Pubmed ID: 15614693 Mycobacterium Abscessus and Children with Cystic Fibrosis Emerging Infectious Diseases. Dec, 2003 | Pubmed ID: 14720400 Use of 16S RRNA Gene Sequencing for Identification of Nonfermenting Gram-negative Bacilli Recovered from Patients Attending a Single Cystic Fibrosis Center Journal of Clinical Microbiology. Oct, 2002 | Pubmed ID: 12354883 Первичные эпителиальные клетки носа человека: биобанкинг в контексте прецизионной медицины Mairead Kelly1,2, Elise Dreano1,2, Aurelie Hatton1,2, Agathe Lepissier1,2, Anita Golec1,2, Isabelle Sermet-Gaudelus1,2,3, Iwona Pranke1,2,3 1Institut Necker Enfants Malades, 2Université de Paris, 3Centre de Référence Maladies Rares Mucoviscidose et Maladies apparentées, Assistance Publique Hôpitaux de Paris JoVE 63409 Biology Стандартные измерения перепада Transepithelial потенциал слизистой (NPD) George M. Solomon1, Inez Bronsveld2, Kathryn Hayes3, Michael Wilschanski4, Paola Melotti5, Steven M. Rowe1, Isabelle Sermet-Gaudelus6,7 1Department of Medicine and the Gregory Fleming James Cystic Fibrosis Center, University of Alabama at Birmingham, 2Department of Pulmonology and Tuberculosis, University Medical Center Utrecht, 3Center for Experimental Medicine, Queens University, Northern Ireland, 4Hadassah Hebrew University Medical Center, Jerusalem, 5Centro Fibrosi Cistica, Azienda Ospedaliera Universitaria Integrata, 6Service de Pneumologie et Allergologie Pédiatriques and Center de Ressources et de Compétence de la Mucoviscidose, Hôpital Necker Enfants Malades, 7INSERM U 1151, Institut Necker Enfants Malades JoVE 57006 Medicine
Первичные эпителиальные клетки носа человека: биобанкинг в контексте прецизионной медицины Mairead Kelly1,2, Elise Dreano1,2, Aurelie Hatton1,2, Agathe Lepissier1,2, Anita Golec1,2, Isabelle Sermet-Gaudelus1,2,3, Iwona Pranke1,2,3 1Institut Necker Enfants Malades, 2Université de Paris, 3Centre de Référence Maladies Rares Mucoviscidose et Maladies apparentées, Assistance Publique Hôpitaux de Paris JoVE 63409 Biology
Стандартные измерения перепада Transepithelial потенциал слизистой (NPD) George M. Solomon1, Inez Bronsveld2, Kathryn Hayes3, Michael Wilschanski4, Paola Melotti5, Steven M. Rowe1, Isabelle Sermet-Gaudelus6,7 1Department of Medicine and the Gregory Fleming James Cystic Fibrosis Center, University of Alabama at Birmingham, 2Department of Pulmonology and Tuberculosis, University Medical Center Utrecht, 3Center for Experimental Medicine, Queens University, Northern Ireland, 4Hadassah Hebrew University Medical Center, Jerusalem, 5Centro Fibrosi Cistica, Azienda Ospedaliera Universitaria Integrata, 6Service de Pneumologie et Allergologie Pédiatriques and Center de Ressources et de Compétence de la Mucoviscidose, Hôpital Necker Enfants Malades, 7INSERM U 1151, Institut Necker Enfants Malades JoVE 57006 Medicine
