Noah Weisleder Davis Heart & Lung Research Institute, Department of Physiology and Cell Biology The Ohio State University Biography Publications Institution JoVE Articles Noah Weisleder has not added a biography. If you are Noah Weisleder and would like to personalize this page please email our Author Liaison for assistance. Publications Novel Excitation-contraction Coupling Related Genes Reveal Aspects of Muscle Weakness Beyond Atrophy-new Hopes for Treatment of Musculoskeletal Diseases Frontiers in Physiology. 2014 | Pubmed ID: 24600395 TRIM Proteins in Therapeutic Membrane Repair of Muscular Dystrophy JAMA Neurology. Jul, 2013 | Pubmed ID: 23699904 A Dual Mode Pulsed Electro-magnetic Cell Stimulator Produces Acceleration of Myogenic Differentiation Recent Patents on Biotechnology. Apr, 2013 | Pubmed ID: 23445453 Type 1 Inositol (1,4,5)-trisphosphate Receptor Activates Ryanodine Receptor 1 to Mediate Calcium Spark Signaling in Adult Mammalian Skeletal Muscle The Journal of Biological Chemistry. Jan, 2013 | Pubmed ID: 23223241 Orai1 Mediates Exacerbated Ca(2+) Entry in Dystrophic Skeletal Muscle PloS One. 2012 | Pubmed ID: 23185465 Poloxamer 188 (p188) As a Membrane Resealing Reagent in Biomedical Applications Recent Patents on Biotechnology. Dec, 2012 | Pubmed ID: 23092436 重组 MG53 蛋白调节治疗细胞膜修复治疗肌营养不良症。 Science Translational Medicine. Jun, 2012 | Pubmed ID: 22723464 加强 MG53 基因交付的肌肉膜修复改善肌营养不良症和心衰的 δ-Sarcoglycan-缺仓鼠。 Molecular Therapy : the Journal of the American Society of Gene Therapy. Feb, 2012 | Pubmed ID: 22314291 非肌细胞肌球蛋白国际投资协定有助于囊泡贩运的 MG53 介导的细胞膜修复。 The FASEB Journal : Official Publication of the Federation of American Societies for Experimental Biology. Jan, 2012 | Pubmed ID: 22253476 检测钙火花完好和透骨骼肌纤维。 Methods in Molecular Biology (Clifton, N.J.). 2012 | Pubmed ID: 22130850 店面式经营钙条目是 HL 1 心肌细胞中存在,并有助于静息钙。 Biochemical and Biophysical Research Communications. Dec, 2011 | Pubmed ID: 22079292 膜结构及与急性组合式的刘斌 1 成人骨骼肌细胞内 Ca²⁺ 信号中断。 PloS One. 2011 | Pubmed ID: 21984944 线粒体钙吸收期间兴奋收缩 (E C) 耦合调节骨骼肌快速钙瞬变。 The Journal of Biological Chemistry. Sep, 2011 | Pubmed ID: 21795684 店面式经营经条目 (赛) 有助于正常骨骼肌收缩力在年轻人中但不是在老年骨骼肌。 Aging. Jun, 2011 | Pubmed ID: 21666285 成像超闪光和代谢耦合线粒体通透中生活的动物。 Cell Research. Sep, 2011 | Pubmed ID: 21556035 氧化还原依赖齐聚亮氨酸拉链母题通过介导 MG53 细胞膜修复至关重要。 American Journal of Physiology. Cell Physiology. Jul, 2011 | Pubmed ID: 21525429 转基因小鼠基因表达的组织特异性和诱导型控制系统多功能单质粒。 FASEB Journal : Official Publication of the Federation of American Societies for Experimental Biology. Aug, 2011 | Pubmed ID: 21518849 Dysferlin、 膜联蛋白 A1,和 Mitsugumin 53 是肌营养不良症的增高,本地化的 T-系统与拉伸的纵向肾小管。 Journal of Neuropathology and Experimental Neurology. Apr, 2011 | Pubmed ID: 21412170 聚合酶逆转录酶释放因子 (PTRF) 定位 MG53 蛋白与膜修复开始的单元格受伤部位。 The Journal of Biological Chemistry. Apr, 2011 | Pubmed ID: 21343302 Junctophilin-2 的表达沉默会导致心肌肥厚和异常的细胞内钙处理。 Circulation. Heart Failure. Mar, 2011 | Pubmed ID: 21216834 两亲性尾锚固肽和 Bcl-2 家族蛋白 Bcl-2 同源域-3 (BH3) 肽通过不同的机制诱导细胞凋亡。 The Journal of Biological Chemistry. Mar, 2011 | Pubmed ID: 21189256 增加减少 Calsequestrin-1 的表达与骨骼肌中的店面式经营 Ca2 + 条目。 Biophysical Journal. Sep, 2010 | Pubmed ID: 20816068 MG53 构成心脏缺血预处理的主要决定因素。 Circulation. Jun, 2010 | Pubmed ID: 20516375 心肌缺血/再灌注损伤的胆固醇依赖 MG53 介导膜修复保护的作用。 Circulation Research. Jul, 2010 | Pubmed ID: 20466981 心脏磷基因表达的镇压介导的甲状腺激素受体-{字母} 1 和涉及有针对性的共价键组蛋白修饰。 Endocrinology. Jun, 2010 | Pubmed ID: 20392835 Junctophilin 2 S165F 突变影响 Ca2 + 信号在骨骼肌中。 The Biochemical Journal. Apr, 2010 | Pubmed ID: 20095964 Mitsugumin 53 (MG53) 有助于囊泡贩运横纹肌有助于细胞膜修复。 Communicative & Integrative Biology. May, 2009 | Pubmed ID: 19641737 肌营养不良症的膜修复缺陷相连 MG53,改变相互作用窖-3 和 Dysferlin。 The Journal of Biological Chemistry. Jun, 2009 | Pubmed ID: 19380584 Bax 的氨基末端肽胞内 Ca2 + 稳态提高前列腺癌细胞凋亡影响了地球。 American Journal of Physiology. Cell Physiology. Feb, 2009 | Pubmed ID: 19091958 MG53 Nucleates 细胞膜修复机械的程序的集。 Nature Cell Biology. Jan, 2009 | Pubmed ID: 19043407 MG53 规管膜萌芽和肌肉细胞中的胞。 The Journal of Biological Chemistry. Jan, 2009 | Pubmed ID: 19029292 结尾巴域链接到人类扩张型心肌病中的错义突变促进劈头域并废除其 Z 盘本地化。 FASEB Journal : Official Publication of the Federation of American Societies for Experimental Biology. Sep, 2008 | Pubmed ID: 18539904 店面式经营 Ca2 + 进入老年骨骼肌中的大打折扣。 Aging Cell. Aug, 2008 | Pubmed ID: 18505477 细胞膜穴样内陷/窖-1 是重要调制器店面式经营钙项在 Hs578/T 乳腺癌中的癌症细胞。 Journal of Pharmacological Sciences. Feb, 2008 | Pubmed ID: 18296864 改变 Ca2 + 老化骨骼肌和心肌的火花。 Ageing Research Reviews. Jul, 2008 | Pubmed ID: 18272434 免疫蛋白质组学对激励 — — 耦合在骨骼肌、 心脏肌肉的收缩: 揭示的 Mitsugumins 分子见解。 Cell Calcium. Jan, 2008 | Pubmed ID: 18061662 Bfl1 和 HCCS1 的目标线粒体膜通透性诱导凋亡的尾锚定域。 Journal of Cell Science. Aug, 2007 | Pubmed ID: 17666431 电位渠道 Ca2 + 在细胞内存储处理至关重要。 Nature. Jul, 2007 | Pubmed ID: 17611541 JPH2 编码 Junctophilin-2 与人类肥厚型心肌病相关的基因突变。 Journal of Molecular and Cellular Cardiology. Jun, 2007 | Pubmed ID: 17509612 RyR3 的系统性消融改变 Ca2 + 成人骨骼肌细胞信号转导的火花。 Cell Calcium. Dec, 2007 | Pubmed ID: 17412417 Azumolene 抑制耦合到骨骼肌兰尼碱受体的店面式经营钙条目的一个组成部分。 The Journal of Biological Chemistry. Nov, 2006 | Pubmed ID: 16945924 肌肉老化是与破坏 Ca2 + 火花信号和隔离胞内 Ca2 + 释放相关联。 The Journal of Cell Biology. Aug, 2006 | Pubmed ID: 16943181 Ca2 + 作为塑料信号的骨骼肌肉健康、 营养不良与老化,火花。 Acta Pharmacologica Sinica. Jul, 2006 | Pubmed ID: 16787561 解偶联店面式经营 Ca2 + 进入和改变 Ca2 + 释放从肌浆网通过 Junctophilin 基因的沉默。 Biophysical Journal. Jun, 2006 | Pubmed ID: 16565048 增强的抗疲劳和改变的钙处理性能的 Sarcalumenin 基因敲除小鼠。 Physiological Genomics. Sep, 2005 | Pubmed ID: 15998745 不受控制的钙火花法 》 作为哺乳动物骨骼肌肉营养不良信号。 Nature Cell Biology. May, 2005 | Pubmed ID: 15834406 心结空心衰模型中线粒体蛋白质组的变化。 Journal of Molecular and Cellular Cardiology. Mar, 2005 | Pubmed ID: 15733906 结蛋白的小鼠骨骼肌被动变形过程的结构和功能的角色。 Biophysical Journal. May, 2004 | Pubmed ID: 15111414 结空型心肌病的心肌细胞特定结救援排除血管介入。 Journal of Molecular and Cellular Cardiology. Jan, 2004 | Pubmed ID: 14734054 Bcl-2 过表达纠正了线粒体缺陷及改良继承的结空型心肌病。 Proceedings of the National Academy of Sciences of the United States of America. Jan, 2004 | Pubmed ID: 14715896 心肌缺血再灌注损伤的通过左前降支结扎小鼠模型 Zhaobin Xu1, Jenna Alloush1, Eric Beck1, Noah Weisleder1 1Davis Heart & Lung Research Institute, Department of Physiology and Cell Biology, The Ohio State University JoVE 51329 Medicine 钙火花的评估在正常肌肉纤维 Ki Ho Park1, Noah Weisleder2, Jingsong Zhou3, Kristyn Gumpper1, Xinyu Zhou1, Pu Duann4, Jianjie Ma1, Pei-Hui Lin1 1Department of Surgery, Davis Heart and Lung Research Institute, The Ohio State University Wexner Medical Center, 2Department of Physiology and Cell Biology, Davis Heart and Lung Research Institute, The Ohio State University Wexner Medical Center, 3Department of Molecular Biophysics and Physiology, Rush University Medical Center, 4Department of Internal Medicine, Davis Heart and Lung Research Institute, The Ohio State University Wexner Medical Center JoVE 50898 Biology MG53介导的细胞膜使用维修的可视化在体内在体外系统 Noah Weisleder1, Peihui Lin1, Xiaoli Zhao1, Matthew Orange1, Hua Zhu1, Jianjie Ma1 1Department of Physiology and Biophysics, Robert Wood Johnson Medical School JoVE 2717 Biology
心肌缺血再灌注损伤的通过左前降支结扎小鼠模型 Zhaobin Xu1, Jenna Alloush1, Eric Beck1, Noah Weisleder1 1Davis Heart & Lung Research Institute, Department of Physiology and Cell Biology, The Ohio State University JoVE 51329 Medicine
钙火花的评估在正常肌肉纤维 Ki Ho Park1, Noah Weisleder2, Jingsong Zhou3, Kristyn Gumpper1, Xinyu Zhou1, Pu Duann4, Jianjie Ma1, Pei-Hui Lin1 1Department of Surgery, Davis Heart and Lung Research Institute, The Ohio State University Wexner Medical Center, 2Department of Physiology and Cell Biology, Davis Heart and Lung Research Institute, The Ohio State University Wexner Medical Center, 3Department of Molecular Biophysics and Physiology, Rush University Medical Center, 4Department of Internal Medicine, Davis Heart and Lung Research Institute, The Ohio State University Wexner Medical Center JoVE 50898 Biology
MG53介导的细胞膜使用维修的可视化在体内在体外系统 Noah Weisleder1, Peihui Lin1, Xiaoli Zhao1, Matthew Orange1, Hua Zhu1, Jianjie Ma1 1Department of Physiology and Biophysics, Robert Wood Johnson Medical School JoVE 2717 Biology