robotic-assisted-lateral-pancreaticojejunostomy-for-chronic

Robotic-assisted Lateral Pancreaticojejunostomy for Chronic Pancreatitis

Chronic pancreatitis is a debilitating, benign inflammatory disorder that significantly alters a patient's quality of life. Pancreatic drainage procedures ...

West Virginia University School of Medicine

We report a 5-year-old girl with transient complete atrioventricular (AV) block following surgical closure of a symptomatic conoventricular ventricular septal defect (VSD) which recovered on post-operative day 9. She later presented with exertional dizziness and fatigue. While congenital cardiac defect repairs are occasionally complicated by complete heart block, this patient was found to have intra-Hisian Wenckebach which is rare in the pediatric population and can be very difficult to discern from surface electrocardiograms and by Holter monitoring. Mechanisms of post-surgical AV block, including intra-Hisian Wenckebach, are not well characterized in the pediatric population.

Intra-Hisian Wenckebach after surgical closure of conoventricular ventricular septal defect.

In a familial cohort with 8 heterozygous carriers of a rare pathogenic  mutation (c.2482C>T), 4 female mutation carriers manifested with fetal ventricular tachycardia and 2:1 atrioventricular block. One presented with multifocal ectopic premature Purkinje-related complexes-like phenotype and atrial fibrillation later in life. These novel findings inform the need for robust fetal monitoring of mutation carriers.

Novel Phenotypic Effects of a Rare  (c.2482C>T) Mutation.

A rare presentation of Ebstein's anomaly: left-sided accessory pathway and tricuspid stenosis.

We report the case of a 16-year-old boy who had myopericarditis following the first dose of a selective androgen receptor modulator called Testolone ("RAD-140"). These drugs are widely abused by physically active young adults; however, the drugs' side effects, which can be life-threatening, are not well characterized.

Myopericarditis Following Use of Selective Androgen Receptor Modifier "RAD-140".

The images presented show heterotaxy (right atrial isomerism), mitral and pulmonary valve atresia, single ventricle physiology, non-confluent branch pulmonary arteries supplied by ipsilateral ductus, and a large VSD. Non-confluent branch pulmonary arteries which are supplied by bilateral ducts are a rare cardiac anomaly which is illustrated by multimodality imaging in this patient.

Article	Year
Intra-Hisian Wenckebach after surgical closure of conoventricular ventricular septal defect. Pacing and clinical electrophysiology : PACE\| PubMed ID: 37938799	2024
Novel Phenotypic Effects of a Rare (c.2482C>T) Mutation. JACC. Case reports\| PubMed ID: 38379642	2024
A rare presentation of Ebstein's anomaly: left-sided accessory pathway and tricuspid stenosis. Journal of interventional cardiac electrophysiology : an international journal of arrhythmias and pacing\| PubMed ID: 38480673	2024
Myopericarditis Following Use of Selective Androgen Receptor Modifier "RAD-140". JACC. Case reports\| PubMed ID: 39157568	2024
Multimodality Imaging of Bilateral Ductus Arteriosus in a Patient With Complex Heterotaxy and a Univentricular Heart. Echocardiography (Mount Kisco, N.Y.)\| PubMed ID: 39912617	2025

Kathryn H. Schwartzman

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