Iwona Pranke

Institut Necker Enfants Malades

Affiliated withInstitut Necker Enfants Malades Université de paris Assistance Publique Hôpitaux de Paris

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JoVE Journal Publications

ArticleTotal : 1	Year
Publication title Cited by 1	2022

Other Publications

Article	Year
An unexpected effect of TNF-α on F508del-CFTR maturation and function. F1000Research\| PubMed ID: 26594334	2015
The suppression of premature termination codons and the repair of splicing mutations in CFTR. Current opinion in pharmacology\| PubMed ID: 29128743	2017
Cis variants identified in F508del complex alleles modulate CFTR channel rescue by small molecules. Human mutation\| PubMed ID: 29271547	2018
Factors influencing readthrough therapy for frequent cystic fibrosis premature termination codons. ERJ open research\| PubMed ID: 29497617	2018
Might Brushed Nasal Cells Be a Surrogate for CFTR Modulator Clinical Response? American journal of respiratory and critical care medicine\| PubMed ID: 30326728	2019
Emerging Therapeutic Approaches for Cystic Fibrosis. From Gene Editing to Personalized Medicine. Frontiers in pharmacology\| PubMed ID: 30873022	2019
Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis. Scientific reports\| PubMed ID: 31019198	2019
Cystic Fibrosis Diagnosis in Newborns, Children, and Adults. Seminars in respiratory and critical care medicine\| PubMed ID: 31679154	2019
Author Correction: Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis. Scientific reports\| PubMed ID: 31754179	2019
Urinary Exosomes of Patients with Cystic Fibrosis Unravel CFTR-Related Renal Disease. International journal of molecular sciences\| PubMed ID: 32927759	2020
Modulators of CFTR. Updates on clinical development and future directions. European journal of medicinal chemistry\| PubMed ID: 33524685	2021
New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation. Scientific reports\| PubMed ID: 33767236	2021
Sweat Chloride Testing and Nasal Potential Difference (NPD) Are Primary Outcome Parameters in Treatment with Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulators. Journal of personalized medicine\| PubMed ID: 34442373	2021
Author Correction: New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation. Scientific reports\| PubMed ID: 34526640	2021
Pharmacological chaperones improve intra-domain stability and inter-domain assembly via distinct binding sites to rescue misfolded CFTR. Cellular and molecular life sciences : CMLS\| PubMed ID: 34714360	2021
Correlating genotype with phenotype using CFTR-mediated whole-cell Cl currents in human nasal epithelial cells. The Journal of physiology\| PubMed ID: 34761808	2022
Systemic bis-phosphinic acid derivative restores chloride transport in Cystic Fibrosis mice. Scientific reports\| PubMed ID: 35413967	2022