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Summary

这项工作提出了一种内皮到间充质转化诱导的纤维化的动物模型,如先天性心脏缺陷,如严重主动脉瓣狭窄或左心发育不良综合征,可以进行详细的组织学组织评估、调节信号通路的鉴定和治疗方案的测试。

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