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Journal
/
Neuroscience
/
ミトコンドリア病モデルのためのヒト脳オルガノイドの生成
JoVE Journal
Neuroscience
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JoVE Journal
Neuroscience
Generation of Human Brain Organoids for Mitochondrial Disease Modeling
Please note that all translations are automatically generated.
Click here for the English version.
ミトコンドリア病モデルのためのヒト脳オルガノイドの生成
DOI:
10.3791/62756-v
•
08:09 min
•
June 21, 2021
•
Stephanie Le
,
Laura Petersilie
,
Gizem Inak
4
,
Carmen Menacho-Pando
,
Karl W. Kafitz
,
Agnieszka Rybak-Wolf
,
Nikolaus Rajewsky
,
Christine R. Rose
,
Alessandro Prigione
5
1
Department of General Pediatrics, Neonatology and Pediatric Cardiology, Duesseldorf University Hospital, Medical Faculty
,
Heinrich Heine University
,
2
Institute of Neurobiology
,
Heinrich Heine University
,
3
Berlin Institute for Medical Systems Biology (BIMSB)
,
Max Delbrueck Center for Molecular Medicine (MDC)
,
4
Seaver Autism Center for Research and Treatment
,
Icahn School of Medicine at Mount Sinai
,
5
Max Delbrueck Center for Molecular Medicine (MDC)
Chapters
00:05
Introduction
00:44
Generation of Brain Organoids
05:31
Immunostaining of Brain Organoids
06:07
Results: Visualization and Bioenergetic Profiling of Brain Organoids Generated from iPSCs
07:34
Conclusion
Summary
Automatic Translation
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Automatic Translation
ヒト誘導多能性幹細胞由来の脳オルガノイドの生成とミトコンドリア病のモデル化におけるその使用に関する詳細なプロトコルについて述べています。
Tags
Brain Organoids
Mitochondrial Diseases
IPSCs
Cortical Differentiation
Neurospheres
ROCK Inhibitor
WNT Inhibitor
SB-431542
Cell Culture
Reproducibility
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